Karaaslan, YaşarÖzbalkan Aşlar, ZeynepCan Sandıkçı, Sevinç2019-05-132019-05-132015Karaaslan, Y., Aslar, Z. O.,Sandıkçı, S. C. (2015). A case with IGG4-related retroperitoneal fibrosis-periaortitis rapidly diagnosed and dramatically responded to steroid treatment. From 8th International Congress of Familial Mediterranean Fever and Systemic Autoinflammatory Diseases Dresden, Germany. 30 September - 3 October 2015.1546-0096https://doi.org/10.1186/1546-0096-13-S1-P2https://hdl.handle.net/11491/1605From 8th International Congress of Familial Mediterranean Fever and Systemic Autoinflammatory Diseases Dresden, Germany. 30 September - 3 October 2015Retroperitoneal fibrosis is a rare disease characterized by development of fibro-inflammatory tissue, which surrounds and causes compression of the retroperitoneal structures such as abdominal aorta, iliac vessels, vena cava and ureters1. It’s prevalence was reported as 1.4 /100,000 2. It has been recently shown that it is one of the IgG4-related disorders3. Herein, we report a male patient who admitted to emergency department with acute abdominal pain, diagnosed with IgG4-related retroperitoneal fibrosis-periaortitis in a very short time, and both high baseline serum creatinine level as well as abdominal pain requiring opioids on admission improved with steroids.enAttribution 4.0 International (CC BY 4.0)info:eu-repo/semantics/openAccess[Belirlenecek]Conference Object13110.1186/1546-0096-13-S1-P2Q2