Colon perforation and Budd-Chiari syndrome in Behçet’s disease
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Tarih
2015
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Medical Science International
Erişim Hakkı
Attribution-NonCommercial-NoDerivatives 4.0 International (CC BY-NC-ND 4.0)
info:eu-repo/semantics/closedAccess
info:eu-repo/semantics/closedAccess
Özet
Objective: Unusual clinical course Background: Behçet’s disease is a chronic inflammatory disease involving multiple systems, with vasculitis being the most important pathological feature. Multiple colon perforations are thought to be secondary to vasculitis and they occur in patients with ulcers. These may be encountered within the entire colon but most commonly in the ileocecal region. Intestinal perforation and Budd-Chiari syndrome are infrequent in Behçet’s disease, and are associated with high mortality and morbidity. Budd-Chiari syndrome results from occlusion of either hepatic veins or adjacent inferior vena cava, or both. Case Report: We report a patient with Behçet’s disease having multiple perforations in the transverse colon, descending colon, and sigmoid colon. The patient also had Budd-Chiari syndrome due to inferior vena cava thrombosis extending into the right and middle hepatic vein. Our observations are presented with a review of the literature. Conclusions: In Behçet’s disease, treatment of colon perforation necessitates urgent surgery, whereas management of Budd- Chiari syndrome is directed towards the underlying cause. Behçet’s disease, as a chronic multisystemic disease with various forms of vasculitis, is resistant to medical and surgical treatment. Prognosis is worse in Behçet’s disease with colon perforation than that in Budd-Chiari syndrome alone. © Am J Case Rep, 2015.
Açıklama
Anahtar Kelimeler
Behcet Syndrome, Budd-Chiari Syndrome, Colorectal Surgery, Intestinal Perforation
Kaynak
American Journal of Case Reports
WoS Q Değeri
N/A
Scopus Q Değeri
Q2
Cilt
16
Sayı
Künye
Baş, Y., Güney, G., Uzbay, P., Zobacı, E., Ardalı, S., Özkan, A. T. (2015). Colon perforation and Budd-Chiari syndrome in Behçet’s disease. American Journal of Case Reports, 16, 262-267.
